Homonymous hemioptic hypoplasia. Fundoscopic features in standard and red-free illumination in three patients with congenital hemiplegia.

Congenital lesions of a cerebral hemisphere may involve its optic tract primarily or trans-synaptically. Such lesions produce a distinctive retrograde hypoplasia in each optic nerve and retina (Fig. I, overleaf) which we have identified ophthalmoscopically and have named homonymous hemioptic hypoplasia. This report describes and illustrates fundoscopic features of this neuro-ophthalmological anomaly viewed in standard and red-free illumination in three Caucasian patients with cerebral hemiatrophy. Each of the three patients was a young epileptic adult with spastic paralysis and underdevelopment of the left arm and leg, left homonymous hemianopia, and the distinctive fundoscopic changes that are the subject of this report. Two of the patients had fixation nystagmus and mildly defective visual acuity (Table I); the amplitude of the nystagmus was greatest on right lateral gaze, and there were Table I Clinical findings in three patients sided congenital hemiplegia with homonymous hemioptic hypoplasia and left-Case No.